Guidelines for physical education teachers in the therapeutic physical approach of schools with Type 1 Glutaric Aciduria: A brief review

  1. González-Loyola, I.
  2. Araneda-Calderón, C.
  3. Valdivia Moral, Pedro Angel
  4. Espinoza-Salinas, A.
  5. Farias-Valenzuela, C.
Aldizkaria:
Education, Sport, Health and Physical Activity (ESHPA): International Journal

ISSN: 2603-6789

Argitalpen urtea: 2022

Alea: 6

Zenbakia: 1

Orrialdeak: 27-38

Mota: Artikulua

DOI: 10.5281/ZENODO.5517196 DIALNET GOOGLE SCHOLAR lock_openDIGIBUG editor

Beste argitalpen batzuk: Education, Sport, Health and Physical Activity (ESHPA): International Journal

Objetivos de desarrollo sostenible

Laburpena

Among the various metabolic alterations in childhood, is Glutaric Aciduria Type 1 (GA-1). This refers to a metabolic disorder of autosomal recessive inheritance and progressive character due to the deficiency of the enzyme glutaryl-CoA-dehydrogenase (GCDH). Affected patients may present cerebral atrophy, macrocephaly and dystonia, pictures that affect autonomy and compromising functional capacity participation in school and social activities. Aim: To identify potential non-pharmacological treatments for the physical-therapeutic approach of GA-1 of boys and girls with orientations towards physical education teachers. Methods: A search was carried out for studies of the type: Meta-analysis, systematic reviews and randomized controlled studies in indexed databases such as: PubMed, Scielo, Scopus and Web of Science. Results & discussion: It is established that assisted physical exercise programs focused on gait pattern, strength, and dynamic and static balance, can be beneficial for the autonomy and functional independence of boys and girls with GA-1. Despite the scant evidence regarding physical therapies and AG-1, it is recommended not to suspend treatments, in order to avoid complications of the disease in childhood. Conclusions: Physical exercise applied by physical education teachers in educational contexts should be considered a complementary therapy to pharmacological and nutritional treatment, it is necessary to design guidelines for the individual and collective approach of school-age boys and girls with GA. -1.

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