Enfermedad de Caroli: a propósito de dos casos

  1. Barrientos-Delgado, Andrés
  2. Florido García, Mónica
  3. del Moral-Martínez, Maria
  4. Casado-Caballero, Francisco Javier
Journal:
Revista andaluza de patología digestiva

ISSN: 1988-317X

Year of publication: 2014

Volume: 37

Issue: 3

Pages: 154-157

Type: Article

More publications in: Revista andaluza de patología digestiva

Abstract

Background and objective Caroli disease (CD) is a congenital condition characterized by the presence of multifocal segmental dilatation of the intrahepatic biliary tracts. Clinically it manifests in younger ages as recurrent cholangitis, hepatolithiasis and liver abscesses, although there are many asymptomatic cases. Patients and method We report two cases of CD which debuted as acute pancreatitis and cholangitis. Results The final diagnosis of CD was established by imaging, magnetic resonance imaging (MRI) being of special interest. Conclusion Despite the rarity of this disease, it is important to keep it in mind when making a differential diagnosis of recurrent cholangitis. Once diagnosed, treatment must be individualized.