AGUSTÍN
HIDALGO GUTIÉRREZ
CONTRATADO DE INVESTIGACIÓN POSTDOCTORAL
ELIANA
BARRIOCANAL CASADO
Investigadora en el periodo 2021-2022
Publicaciones en las que colabora con ELIANA BARRIOCANAL CASADO (12)
2024
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Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease
Annals of Neurology
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Oral β-RA induces metabolic rewiring leading to the rescue of diet-induced obesity
Biochimica et Biophysica Acta - Molecular Basis of Disease, Vol. 1870, Núm. 7
2022
2021
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Animal models of coenzyme q deficiency: Mechanistic and translational learnings
Antioxidants, Vol. 10, Núm. 11
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Metabolic targets of coenzyme q10 in mitochondria
Antioxidants, Vol. 10, Núm. 4
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β-RA Targets Mitochondrial Metabolism and Adipogenesis, Leading to Therapeutic Benefits against CoQ Deficiency and Age-Related Overweight
Biomedicines, Vol. 9, Núm. 10
2020
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Coenzyme Q10 modulates sulfide metabolism and links the mitochondrial respiratory chain to pathways associated to one carbon metabolism
Human Molecular Genetics, Vol. 29, Núm. 19, pp. 3296-3311
2019
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β-RA reduces DMQ/CoQ ratio and rescues the encephalopathic phenotype in Coq9 R239X mice
EMBO Molecular Medicine, Vol. 11, Núm. 1
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Rapamycin administration is not a valid therapeutic strategy for every case of mitochondrial disease
EBioMedicine, Vol. 42, pp. 511-523
2018
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Reduction in the levels of CoQ biosynthetic proteins is related to an increase in lifespan without evidence of hepatic mitohormesis
Scientific Reports, Vol. 8, Núm. 1
2017
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CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndrome
EMBO Molecular Medicine, Vol. 9, Núm. 1, pp. 78-95